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semantic dementia

progressive neurodegenerative disorder
Class type of: behavioral variant of frontotemporal dementia, progressive nonfluent aphasia Q18587

Facts

7 properties
Instance of
class of disease
Subclass of
behavioral variant of frontotemporal dementia, progressive nonfluent aphasia[2][3]
Age of onset
adult onset[13]
Genetic association
MAPT, GRN, PSEN1, TREM2, TMEM106B, CHMP2B, C9orf72[6][7][8][9][10][11][12]
Has phenotype
aphasia, Middle age onset, brain atrophy, visual agnosia, anomic aphasia, amyotrophic lateral sclerosis, dementia, speech disorder, dyslexia, visual verbal agnosia, dysgraphia, aboulia, parkinsonian syndrome[14][15][16][17][18][19][20][21][22][23][24][25][26]
Health specialty
neurology[5]
Prevalence
+0.000001[4]
🏷️ Also known as
en Semantic variant PPA en Wilhelmsen-Lynch Disease en Dementia, Frontotemporal, With Parkinsonism en Disinhibition-Dementia-Parkinsonism-Amyotrophy Complex en FRONTOTEMPORAL DEMENTIA en FRONTOTEMPORAL DEMENTIA; FTD en Frontotemporal Dementia With Parkinsonism en Frontotemporal Lobar Degeneration With Tau Inclusions en Frontotemporal Lobe Dementia en FTD en Ftdp17 en Ftld With Tau Inclusions en Multiple System Tauopathy With Presenile Dementia en Pallidopontonigral Degeneration en Pick Complex en semantic dementia en Semantic primary progressive aphasia ar خرف دلالة الرموز de Semantische Demenz es demencia semantica
🔖 Identifiers · 14
OpenAlex ID
C2779116556
Exact match
www.orpha.net
Freebase ID
/m/06xs_3
GARD rare disease ID
10792
GeneReviews ID
NBK1505
Human Phenotype Ontology ID
HP:0030219
ICD-10-CM
G31.0
ICD-9 ID
331.19
Microsoft Academic ID (discontinued)
2779116556
Mondo ID
MONDO_0010857
OMIM ID
600274
Orphanet ID
100069
Show all 14 identifiers +2
Raras disease ID
D100069
UMLS CUI
C0338462, C0338451, C1838313, C1862937

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🔗 Connections
Health specialty 1
neurology
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Summary

semantic dementia is a class of disease[1].

Related Entities

neurology

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  2. [3] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  3. [4] ↑ . Retrieved . wikidata.org.
  4. [5] ↑ . wikidata.org.
  5. [6] ↑ . Open Targets Platform. Retrieved . platform.opentargets.org. Provenance: wikidata.org.
  6. [7] ↑ . Retrieved . wikidata.org.
  7. [8] ↑ . Retrieved . wikidata.org.
  8. [9] ↑ . Retrieved . wikidata.org.
  9. [10] ↑ . Retrieved . wikidata.org.
  10. [11] ↑ . Retrieved . wikidata.org.
  11. [12] ↑ . Retrieved . wikidata.org.
  12. [13] ↑ . Retrieved . wikidata.org.
  13. [14] ↑ . Retrieved . wikidata.org.
  14. [15] ↑ . Retrieved . wikidata.org.
  15. [16] ↑ . Retrieved . wikidata.org.
  16. [17] ↑ . Retrieved . wikidata.org.
  17. [18] ↑ . Retrieved . wikidata.org.
  18. [19] ↑ . Retrieved . wikidata.org.
  19. [20] ↑ . Retrieved . wikidata.org.
  20. [21] ↑ . Retrieved . wikidata.org.
  21. [22] ↑ . Retrieved . wikidata.org.
  22. [23] ↑ . Retrieved . wikidata.org.
  23. [24] ↑ . Retrieved . wikidata.org.
  24. [25] ↑ . Retrieved . wikidata.org.
  25. [26] ↑ . Retrieved . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). semantic dementia. Retrieved November 12, 2026, from https://4ort.xyz/entity/semantic-dementia
MLA “semantic dementia.” 4ort.xyz Knowledge Graph, 4ort.xyz, 12 Nov. 2026, https://4ort.xyz/entity/semantic-dementia.
BibTeX @misc{4ortxyz_semantic-dementia_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{semantic dementia}}, year = {2026}, url = {https://4ort.xyz/entity/semantic-dementia}, note = {Accessed: 2026-11-12}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): semantic dementia — https://4ort.xyz/entity/semantic-dementia (retrieved 2026-11-12)

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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 20d ago · ACorrêa (WMB) · 2026-10-23 view diff on Wikidata ↗
    Instance of → class of disease
    Health specialty → neurology
    Genetic association → MAPT, GRN, PSEN1 +1
    Prevalence → 0.000001
    + 4 other properties edited (see Wikidata diff for full list)
    "Changed the item: QuickStatements 3.0 batch #61469: Raras.org data import"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.