arrhythmogenic right ventricular cardiomyopathy
intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle
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Summary
arrhythmogenic right ventricular cardiomyopathy is a rare disease[1]. It draws 1,898 Wikipedia views per month (rare disease category, ranking #160 of 627).[2]
Key Facts
- Instance of: class of disease[3]
- Subclass of: intrinsic cardiomyopathy[4], genetic cardiac disease[5]
- Commons category: Arrhythmogenic right ventricular cardiomyopathy[6]
- Prevalence: 0.0003[7]
- ICD-9-CM: 425.4[8]
- NCI Thesaurus ID: C84571[9]
- Health specialty: cardiology[10]
- Genetic association: TGFB3[11], DSG2[12], PKP2[13], JUP[14], DSP[15], DSC2[16], RYR2[17], CDH2[18], CTNNA3[19], LMNA[20], PLN[21], TTN[22], LDB3[23], TMEM43[24]
- Age of onset: juvenile onset[25], adult onset[26]
- Exact match: http://purl.obolibrary.org/obo/DOID_0050431[27], http://identifiers.org/doid/DOID:0050431[28], http://www.orpha.net/ORDO/Orphanet_217656[29], http://www.orpha.net/ORDO/Orphanet_247[30]
- On focus list of Wikimedia project: WikiProject Medicine[31]
- P14914: D00247[32]
Why It Matters
arrhythmogenic right ventricular cardiomyopathy has Wikipedia articles in 11 language editions, a strong signal of global cultural recognition.[33] It is known by 47 alternative names across languages and contexts.[34]