paroxysmal nocturnal hemoglobinuria

disease of the blood characterized by destruction of red blood cells by the complement system, a part of the body's innate immune system
MedicalCondition designated_intractable_rare_disease Q1479494
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paroxysmal nocturnal hemoglobinuria

Summary

paroxysmal nocturnal hemoglobinuria is a designated intractable/rare disease[1]. It draws 592 Wikipedia views per month (designated_intractable_rare_disease category, ranking #99 of 201).[2]

Key Facts

  • paroxysmal nocturnal hemoglobinuria's instance of is recorded as designated intractable/rare disease[3].
  • paroxysmal nocturnal hemoglobinuria's instance of is recorded as rare disease[4].
  • paroxysmal nocturnal hemoglobinuria's instance of is recorded as class of disease[5].
  • Ettore Marchiafava is named after paroxysmal nocturnal hemoglobinuria[6].
  • Ferdinando Micheli is named after paroxysmal nocturnal hemoglobinuria[7].
  • paroxysmal nocturnal hemoglobinuria is a type of hemoglobinuria[8].
  • paroxysmal nocturnal hemoglobinuria is a type of disease[9].
  • paroxysmal nocturnal hemoglobinuria's external data available at URL is recorded as http://www.nanbyou.or.jp/entry/3783[10].
  • paroxysmal nocturnal hemoglobinuria's NCI Thesaurus ID is recorded as C61233[11].
  • paroxysmal nocturnal hemoglobinuria's health specialty is recorded as hematology[12].
  • paroxysmal nocturnal hemoglobinuria's drug or therapy used for treatment is recorded as eculizumab[13].
  • paroxysmal nocturnal hemoglobinuria's genetic association is recorded as PIGT[14].
  • paroxysmal nocturnal hemoglobinuria's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0060284[15].
  • paroxysmal nocturnal hemoglobinuria's exact match is recorded as http://identifiers.org/doid/DOID:0060284[16].
  • paroxysmal nocturnal hemoglobinuria's exact match is recorded as http://purl.obolibrary.org/obo/HP_0004818[17].
  • paroxysmal nocturnal hemoglobinuria's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_447[18].
  • paroxysmal nocturnal hemoglobinuria's on focus list of Wikimedia project is recorded as WikiProject Medicine[19].

Why It Matters

paroxysmal nocturnal hemoglobinuria draws 592 Wikipedia views per month (designated_intractable_rare_disease category, ranking #99 of 201).[2] It has Wikipedia articles in 19 language editions, a strong signal of global cultural recognition.[20] It is known by 29 alternative names across languages and contexts.[21]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . ddrare.nibiohn.go.jp. Retrieved . ddrare.nibiohn.go.jp. Provenance: wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . wikidata.org.
  4. [6] . wikidata.org.
  5. [7] . wikidata.org.
  6. [8] . Disease Ontology. Retrieved . wikidata.org.
  7. [9] . wikidata.org.
  8. [10] . ddrare.nibiohn.go.jp. Retrieved . ddrare.nibiohn.go.jp. Provenance: wikidata.org.
  9. [11] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  10. [12] . wikidata.org.
  11. [13] . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  12. [14] . A case of paroxysmal nocturnal hemoglobinuria caused by a germline mutation and a somatic mutation in PIGT.. wikidata.org.
  13. [15] . Disease Ontology. Retrieved . wikidata.org.
  14. [16] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  15. [17] . Human Phenotype Ontology release 2018-03-08. Retrieved . wikidata.org.
  16. [18] . wikidata.org.
  17. [19] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.
  2. [20] . Wikidata sitelinks. wikidata.org.
  3. [21] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). paroxysmal nocturnal hemoglobinuria. Retrieved May 3, 2026, from https://4ort.xyz/entity/paroxysmal-nocturnal-hemoglobinuria
MLA “paroxysmal nocturnal hemoglobinuria.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/paroxysmal-nocturnal-hemoglobinuria.
BibTeX @misc{4ortxyz_paroxysmal-nocturnal-hemoglobinuria_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{paroxysmal nocturnal hemoglobinuria}}, year = {2026}, url = {https://4ort.xyz/entity/paroxysmal-nocturnal-hemoglobinuria}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): paroxysmal nocturnal hemoglobinuria — https://4ort.xyz/entity/paroxysmal-nocturnal-hemoglobinuria (retrieved 2026-05-03)

Canonical URL: https://4ort.xyz/entity/paroxysmal-nocturnal-hemoglobinuria · Last refreshed:

Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 19d ago · Comfyquiettree · 2026-06-07 view diff on Wikidata ↗
    Wikiskripta article id 8240
    "/* wbsetclaim-create:1||1 */ [[Property:P3471]]: 8240, Matched to [[:toollabs:mix-n-match/#/entry/78315596|Paroxysmální noční hemoglobinurie (#78315596)]] in [[:toollabs:mix-n-match/#/catalog/2686|Wik"
  2. 4w ago · Twofivesixbot bot · 2026-05-27 view diff on Wikidata ↗
    Health specialty hematology
    Instance of designated intractable/rare disease, rare disease, class of disease
    Subclass of
    Aliases
    + 7 other properties edited (see Wikidata diff for full list)
    "/* wbsetclaim-update-qualifiers:1||1|2 */ [[Property:P8189]]: 987007537356905171, mv to monolingual text names on J9U statements"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.