infantile cerebellar-retinal degeneration

neurodegenerative disease that is characterized by onset between ages 2 and 6 months of truncal hypotonia, athetosis, seizures, and ophthalmologic abnormalities, particularly optic atrophy and retinal degeneration
MedicalCondition rare_disease Q18553533
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infantile cerebellar-retinal degeneration

Summary

infantile cerebellar-retinal degeneration is a rare disease[1].

Key Facts

  • infantile cerebellar-retinal degeneration's instance of is recorded as rare disease[2].
  • infantile cerebellar-retinal degeneration's instance of is recorded as class of disease[3].
  • infantile cerebellar-retinal degeneration is a type of neurodegeneration[4].
  • infantile cerebellar-retinal degeneration is a type of eye degenerative disease[5].
  • infantile cerebellar-retinal degeneration is a type of nervous system heredodegenerative disease[6].
  • infantile cerebellar-retinal degeneration is a type of neurometabolic disease[7].
  • infantile cerebellar-retinal degeneration is a type of hereditary retinal dystrophy[8].
  • infantile cerebellar-retinal degeneration is a type of tricarboxylic acid cycle disorder[9].
  • infantile cerebellar-retinal degeneration is a type of autosomal recessive disease[10].
  • infantile cerebellar-retinal degeneration's symptoms and signs is recorded as retinal degeneration[11].
  • infantile cerebellar-retinal degeneration's symptoms and signs is recorded as neonatal hypotonia[12].
  • infantile cerebellar-retinal degeneration's genetic association is recorded as ACO2[13].
  • infantile cerebellar-retinal degeneration's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0050883[14].
  • infantile cerebellar-retinal degeneration's exact match is recorded as http://identifiers.org/doid/DOID:0050883[15].
  • infantile cerebellar-retinal degeneration's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_313850[16].
  • infantile cerebellar-retinal degeneration's on focus list of Wikimedia project is recorded as WikiProject Medicine[17].

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] . wikidata.org.
  2. [3] . wikidata.org.
  3. [4] . Disease Ontology. Retrieved . wikidata.org.
  4. [5] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  5. [6] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [9] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  9. [10] . Disease Ontology. Retrieved . wikidata.org.
  10. [11] . Purkinje cell degeneration, a new neurological mutation in the mouse. wikidata.org.
  11. [12] . Loss of tubulin deglutamylase CCP1 causes infantile-onset neurodegeneration. wikidata.org.
  12. [13] . Q905695. Retrieved . platform.opentargets.org. Provenance: wikidata.org.
  13. [14] . Disease Ontology. Retrieved . wikidata.org.
  14. [15] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  15. [16] . wikidata.org.
  16. [17] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). infantile cerebellar-retinal degeneration. Retrieved May 3, 2026, from https://4ort.xyz/entity/infantile-cerebellar-retinal-degeneration
MLA “infantile cerebellar-retinal degeneration.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/infantile-cerebellar-retinal-degeneration.
BibTeX @misc{4ortxyz_infantile-cerebellar-retinal-degeneration_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{infantile cerebellar-retinal degeneration}}, year = {2026}, url = {https://4ort.xyz/entity/infantile-cerebellar-retinal-degeneration}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): infantile cerebellar-retinal degeneration — https://4ort.xyz/entity/infantile-cerebellar-retinal-degeneration (retrieved 2026-05-03)

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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 2d ago · JhealdBatch bot · 2026-07-05 view diff on Wikidata ↗
    Mondo id MONDO_0013802
    Imported from
    Umls cui C3281192
    Disease ontology id DOID:0050883
    + 13 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39953|batch #39953]]: deprecate redundant disease superclasses (2)"
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