Denys-Drash syndrome

Human disease
MedicalCondition rare_disease Q774016
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Summary

Denys-Drash syndrome is a rare disease[1]. It draws 209 Wikipedia views per month (rare disease category, ranking #114 of 627).[2]

Key Facts

  • Instance of: class of disease[3]
  • Named after: Pierre Denys[4], Allan L. Drash[5]
  • Subclass of: autosomal dominant disease[6], nephroblastoma[7], pseudohermaphroditism[8], primary glomerular disease[9], syndrome with disorder of sex development of gynecological interest[10], polymalformative genetic syndrome with increased risk of developing cancer[11], syndrome with 46,XY disorder of sex development[12], syndrome[13], developmental defect during embryogenesis[14]
  • ICD-9-CM: 189.0[15]
  • NCI Thesaurus ID: C84668[16]
  • Health specialty: oncology[17], endocrinology[18], urology[19], obstetrics and gynaecology[20], medical genetics[21]
  • Genetic association: WT1[22]
  • Exact match: http://purl.obolibrary.org/obo/DOID_3764[23], http://identifiers.org/doid/DOID:3764[24], http://www.orpha.net/ORDO/Orphanet_220[25]
  • On focus list of Wikimedia project: WikiProject Medicine[26]

Why It Matters

Denys-Drash syndrome has Wikipedia articles in 8 language editions, a strong signal of global cultural recognition.[27] It is known by 19 alternative names across languages and contexts.[28]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] ↑ . wikidata.org.
  2. [4] ↑ . wikidata.org.
  3. [5] ↑ . wikidata.org.
  4. [6] ↑ . Disease Ontology. Retrieved . wikidata.org.
  5. [7] ↑ . wikidata.org.
  6. [8] ↑ . wikidata.org.
  7. [9] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [10] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  9. [11] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  10. [12] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  11. [13] ↑ . Disease Ontology. Retrieved . wikidata.org.
  12. [14] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  13. [15] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  14. [16] ↑ . Disease Ontology. Retrieved . wikidata.org.
  15. [17] ↑ . wikidata.org.
  16. [18] ↑ . wikidata.org.
  17. [19] ↑ . wikidata.org.
  18. [20] ↑ . wikidata.org.
  19. [21] ↑ . wikidata.org.
  20. [22] ↑ . UniProt. Retrieved . search.clinicalgenome.org. Provenance: wikidata.org.
  21. [23] ↑ . Disease Ontology. Retrieved . wikidata.org.
  22. [24] ↑ . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  23. [25] ↑ . wikidata.org.
  24. [26] ↑ . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] ↑ . Wikimedia Foundation. dumps.wikimedia.org.
  2. [27] ↑ . Wikidata sitelinks. wikidata.org.
  3. [28] ↑ . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Denys-Drash syndrome. Retrieved October 14, 2026, from https://4ort.xyz/entity/denys-drash-syndrome
MLA “Denys-Drash syndrome.” 4ort.xyz Knowledge Graph, 4ort.xyz, 14 Oct. 2026, https://4ort.xyz/entity/denys-drash-syndrome.
BibTeX @misc{4ortxyz_denys-drash-syndrome_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Denys-Drash syndrome}}, year = {2026}, url = {https://4ort.xyz/entity/denys-drash-syndrome}, note = {Accessed: 2026-10-14}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Denys-Drash syndrome — https://4ort.xyz/entity/denys-drash-syndrome (retrieved 2026-10-14)

Canonical URL: https://4ort.xyz/entity/denys-drash-syndrome · Last refreshed:

Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 8d ago · Tymewalk · 2026-10-08 view diff on Wikidata ↗
    Miraheze article id → lgbta:Denys-Drash_Syndrome
    Wikipedia languages → ['ar', 'bs', 'de', 'en', 'fa', 'fi', 'fr', 'it', 'ml', 'pl']
    Claims rich → —
    "/* wbsetclaim-create:1||1 */ Miraheze article id: lgbta:Denys-Drash_Syndrome, Matched to [[:toollabs:mix-n-match/#/entry/327232170|Denys-Drash Syndrome (#327232170)]] in [[:toollabs:mix-n-match/#/cata"
  2. 15w ago · JhealdBatch bot · 2026-07-03 view diff on Wikidata ↗
    Subclass of → autosomal dominant disease, nephroblastoma, pseudohermaphroditism +6
    Named after → —
    Health specialty → oncology, endocrinology, urology +2
    Genetic association → WT1
    + 6 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39742|batch #39742]]: subclass of disease, not instance"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.